Retina-Vitreous
2010 , Vol 18 , Num 3
Rare Congenital Retinal Vascular Anomalies
1Ufuk Üniversitesi Göz Hastalıkları A.D., Ankara, Doç. Dr.2Ufuk Üniversitesi Göz Hastalıkları A.D., Ankara, Yard. Doç. Dr.
3Ufuk Üniversitesi Göz Hastalıkları A.D., Ankara, Asist. Dr.
4Ufuk Üniversitesi Göz Hastalıkları A.D. Ankara, Prof. Dr. Purpose: To define clinical and demographic findings of congenital retinal vascular anomalies and to review the characteristic signs useful to make differential diagnosis.
Materials and Methods: Cases with detected congenital retinal vascular anomalies were evaluated via detailed ophthalmic examination, fundus photography, flouresceine angiography and also associated systemic diseases were investigated.
Results: The study comprised 25 eyes of 15 patients with congenital retinal vascular anomalies that had complete systemic examinations. Congenital retinal arterial tortuosity was found in 5 cases, prepapillary vascular loops was observed in 4 eyes, macular macro-vessel was discovered in 1 eye, idiopathic generalized tortuosity was detected in 5 cases. No complications that could be pertained to vascular anomalies was observed except two patients in whom one eye with idiopathic generalized tortuosity had associated branch retinal vein occlusion and both eyes of a patient with bilateral congenital retinal arterial tortuosity was accompanied by maculopathy.
Conclusion: Congenital retinal arterial tortuosity, prepapillary vascular loops, macular macro-vessels and idiopathic generalized tortuosity are among congenital retinal vascular anomalies that have favorable prognosis and infrequent complications. Differentiating these anomalies from systemic and ocular conditions that may lead to similar findings is useful in diagnosis and follow-up of these patients. Keywords : Arterial tortuosity, venous tortuosity, prepapillary loop, macro-vessel